What is Usher Syndrome?

Usher Syndrome is a genetic condition characterized by deafness at birth or progressive hearing loss and progressive vision loss.

Symptoms of Usher Syndrome type 1:

  • Bilateral profound deafness from birth
  • Vestibular (balance) problems from birth that can include
    • Poor head control as an infant
    • Arching of back as an infant
    • Late sitting
    • Late walking at age 18 months or later and then with poor balance for the first few years
    • Decreasing night vision beginning in childhood to adolescence

For more information on Usher Syndrome, visit the NIDCD website.